Acute Respiratory Distress and Failure in the Patient with Cystic Fibrosis
In this video, Dr. Emily Barsky reviews the clinical presentation of respiratory distress in patients with cystic fibrosis and lists interventions for a patient with this diagnosis.

Learning Objectives
Recall essential airway and intubation equipment that must be immediately available when managing patients with worsening respiratory distress or impending respiratory failure
Explain how clinical findings such as altered mental status, severe work of breathing, hypercarbia, or hypoxia inform preparation for advanced airway management
Apply systematic setup and readiness checks of intubation equipment in response to escalating respiratory compromise in a simulated or clinical environment
Analyze patient presentation and physiologic data to determine when intubation equipment setup and airway escalation are indicated versus continued non‑invasive support
Evaluate the appropriateness and safety of intubation equipment selection and readiness based on patient condition and predicted airway difficulty
Author(s)
Emily Barsky, MD, MBE
Pediatric Associate Director, Cystic Fibrosis Center | Boston Children's Hospital
Pulmonologist, Division of Pulmonary Medicine | Boston Children's Hospital
Instructor of Pediatrics | Harvard Medical School
Mollie Grunat
Resident Doctor | Thomas Jefferson University Hospitals
Brittanie Marques, BFA
Sr. Medical Illustrator and Animator | OPENPediatrics | Boston Children's Hospital
Katherine R. Schlosser Metitri, MD
Pediatric Critical Care Specialist | Columbia University
Vice President, Operations | NewYork-Presbyterian Morgan Stanley Children’s Hospital
Citation
Barsky E, Grunat MS, Marques B, Schlosser K. Acute Respiratory Distress and Failure in the Patient with Cystic Fibrosis. 10/2019. Online Video. OPENPediatrics. https://learn.openpediatrics.org/learn/course/internal/view/elearning/2958/acute-respiratory-distress-and-failure-in-the-patient-with-cystic-fibrosis.
